Abstract：This paper mainly discusses the different manifestations, clinical diagnosis and treatment of commonly seen congenital long-QT syndrome. The past two decades has witnessed dramatic changes of its treatment. This paper gives a brief introduction to its risk stratification and screening of suspected patients, and also provides suggestions for young athletes with LQTS. For the cases with a medical history of syncope or convulsion, especially with a family history of inexplicable sudden death among firstdegree relatives, LQTS-related examination and diagnosis should be recommended. The treatment for congenital LQTS includes changes of life style, and rational drug and non-drug therapies.
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2016, Vol. 25 
